Disorders involving the immune mechanism
279
Endocrine/metabolic
Both
279-279.99
ICD mappings
| ICD code | Type | Description | Phenome |
|---|---|---|---|
| D80.0 | ICD10CM | Hereditary hypogammaglobulinemia | MGI |
| D80.1 | ICD10CM | Nonfamilial hypogammaglobulinemia | MGI |
| D80.2 | ICD10CM | Selective deficiency of immunoglobulin A [IgA] | MGI |
| D80.3 | ICD10CM | Selective deficiency of immunoglobulin G [IgG] subclasses | MGI |
| D80.4 | ICD10CM | Selective deficiency of immunoglobulin M [IgM] | MGI |
| D80.5 | ICD10CM | Immunodeficiency with increased immunoglobulin M [IgM] | MGI |
| D80.6 | ICD10CM | Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia | MGI |
| D80.7 | ICD10CM | Transient hypogammaglobulinemia of infancy | MGI |
| D80.8 | ICD10CM | Other immunodeficiencies with predominantly antibody defects | MGI |
| D80.9 | ICD10CM | Immunodeficiency with predominantly antibody defects, unspecified | MGI |
| D81 | ICD10CM | Combined immunodeficiencies | MGI |
| D81.0 | ICD10CM | Severe combined immunodeficiency [SCID] with reticular dysgenesis | MGI |
| D81.1 | ICD10CM | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers | MGI |
| D81.2 | ICD10CM | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers | MGI |
| D81.3 | ICD10CM | Adenosine deaminase [ADA] deficiency | MGI |
| D81.4 | ICD10CM | Nezelof's syndrome | MGI |
| D81.5 | ICD10CM | Purine nucleoside phosphorylase [PNP] deficiency | MGI |
| D81.6 | ICD10CM | Major histocompatibility complex class I deficiency | MGI |
| D81.7 | ICD10CM | Major histocompatibility complex class II deficiency | MGI |
| D81.8 | ICD10CM | Other combined immunodeficiencies | MGI |
| D81.81 | ICD10CM | Biotin-dependent carboxylase deficiency | MGI |
| D81.810 | ICD10CM | Biotinidase deficiency | MGI |
| D81.818 | ICD10CM | Other biotin-dependent carboxylase deficiency | MGI |
| D81.819 | ICD10CM | Biotin-dependent carboxylase deficiency, unspecified | MGI |
| D81.89 | ICD10CM | Other combined immunodeficiencies | MGI |
| D81.9 | ICD10CM | Combined immunodeficiency, unspecified | MGI |
| D82.0 | ICD10CM | Wiskott-Aldrich syndrome | MGI |
| D82.1 | ICD10CM | Di George's syndrome | MGI |
| D82.2 | ICD10CM | Immunodeficiency with short-limbed stature | MGI |
| D82.3 | ICD10CM | Immunodeficiency following hereditary defective response to Epstein-Barr virus | MGI |
| D82.4 | ICD10CM | Hyperimmunoglobulin E [IgE] syndrome | MGI |
| D82.8 | ICD10CM | Immunodeficiency associated with other specified major defects | MGI |
| D82.9 | ICD10CM | Immunodeficiency associated with major defect, unspecified | MGI |
| D83 | ICD10CM | Common variable immunodeficiency | MGI |
| D83.0 | ICD10CM | Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function | MGI |
| D83.1 | ICD10CM | Common variable immunodeficiency with predominant immunoregulatory T-cell disorders | MGI |
| D83.2 | ICD10CM | Common variable immunodeficiency with autoantibodies to B- or T-cells | MGI |
| D83.8 | ICD10CM | Other common variable immunodeficiencies | MGI |
| D83.9 | ICD10CM | Common variable immunodeficiency, unspecified | MGI |
| D84.0 | ICD10CM | Lymphocyte function antigen-1 [LFA-1] defect | MGI |
| D84.8 | ICD10CM | Other specified immunodeficiencies | MGI |
| D84.9 | ICD10CM | Immunodeficiency, unspecified | MGI |
| D89.3 | ICD10CM | Immune reconstitution syndrome | MGI |
| D89.82 | ICD10CM | Autoimmune lymphoproliferative syndrome [ALPS] | MGI |
| D89.89 | ICD10CM | Other specified disorders involving the immune mechanism, not elsewhere classified | MGI |
| D89.9 | ICD10CM | Disorder involving the immune mechanism, unspecified | MGI |
| 279.00 | ICD9CM | Hypogammaglobulinemia, unspecified | MGI |
| 279.01 | ICD9CM | Selective IgA immunodeficiency | MGI |
| 279.02 | ICD9CM | Selective IgM immunodeficiency | MGI |
| 279.03 | ICD9CM | Other selective immunoglobulin deficiencies | MGI |
| 279.04 | ICD9CM | Congenital hypogammaglobulinemia | MGI |
| 279.05 | ICD9CM | Immunodeficiency with increased IgM | MGI |
| 279.06 | ICD9CM | Common variable immunodeficiency | MGI |
| 279.09 | ICD9CM | Other deficiency of humoral immunity | MGI |
| 279.10 | ICD9CM | Immunodeficiency with predominant T-cell defect, unspecified | MGI |
| 279.11 | ICD9CM | Digeorge's syndrome | MGI |
| 279.12 | ICD9CM | Wiskott-aldrich syndrome | MGI |
| 279.13 | ICD9CM | Nezelof's syndrome | MGI |
| 279.19 | ICD9CM | Other deficiency of cell-mediated immunity | MGI |
| 279.2 | ICD9CM | Combined immunity deficiency | MGI |
| 279.3 | ICD9CM | Unspecified immunity deficiency | MGI |
| 279.41 | ICD9CM | Autoimmune lymphoproliferative syndrome | MGI |
| 279.49 | ICD9CM | Autoimmune disease, not elsewhere classified | MGI |
| 279.8 | ICD9CM | Other specified disorders involving the immune mechanism | MGI |
| 279.9 | ICD9CM | Unspecified disorder of immune mechanism | MGI |
| D80.0 | ICD10 | D80.0 Hereditary hypogammaglobulinaemia | UKB |
| D80.1 | ICD10 | D80.1 Nonfamilial hypogammaglobulinaemia | UKB |
| D80.2 | ICD10 | D80.2 Selective deficiency of immunoglobulin A [IgA] | UKB |
| D80.3 | ICD10 | D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses | UKB |
| D80.4 | ICD10 | D80.4 Selective deficiency of immunoglobulin M [IgM] | UKB |
| D80.5 | ICD10 | D80.5 Immunodeficiency with increased immunoglobulin M [IgM] | UKB |
| D80.6 | ICD10 | D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia | UKB |
| D80.8 | ICD10 | D80.8 Other immunodeficiencies with predominantly antibody defects | UKB |
| D80.9 | ICD10 | D80.9 Immunodeficiency with predominantly antibody defects, unspecified | UKB |
| D81.0 | ICD10 | D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis | UKB |
| D81.1 | ICD10 | D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers | UKB |
| D81.8 | ICD10 | D81.8 Other combined immunodeficiencies | UKB |
| D81.9 | ICD10 | D81.9 Combined immunodeficiency, unspecified | UKB |
| D82.1 | ICD10 | D82.1 Di George's syndrome | UKB |
| D82.3 | ICD10 | D82.3 Immunodeficiency following hereditary defective response to Epstein-Barr virus | UKB |
| D82.4 | ICD10 | D82.4 Hyperimmunoglobulin E [IgE] syndrome | UKB |
| D82.9 | ICD10 | D82.9 Immunodeficiency associated with major defect, unspecified | UKB |
| D83.0 | ICD10 | D83.0 Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function | UKB |
| D83.1 | ICD10 | D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders | UKB |
| D83.2 | ICD10 | D83.2 Common variable immunodeficiency with autoantibodies to B- or T-cells | UKB |
| D83.8 | ICD10 | D83.8 Other common variable immunodeficiencies | UKB |
| D83.9 | ICD10 | D83.9 Common variable immunodeficiency, unspecified | UKB |
| D84.0 | ICD10 | D84.0 Lymphocyte function antigen-1 [LFA-1] defect | UKB |
| D84.8 | ICD10 | D84.8 Other specified immunodeficiencies | UKB |
| D84.9 | ICD10 | D84.9 Immunodeficiency, unspecified | UKB |
| D89.8 | ICD10 | D89.8 Other specified disorders involving the immune mechanism, not elsewhere classified | UKB |
| D89.9 | ICD10 | D89.9 Disorder involving the immune mechanism, unspecified | UKB |
| 279 | ICD9 | 279 Disorders involving the immune mechanism | UKB |
| 279.9 | ICD9 | 2799 Unspecified disorders involving the immune mechanism | UKB |
This page is mainly a phenotype dictionary entry. When you are trying to find candidate PRS models, go to the Scores table, search by trait or exposure name, and then use the score-detail and PheWAS pages for model-specific follow-up.