Departments of Anesthesiology and Biostatistics | University of Michigan

ICD mappings

ICD code Type Description Phenome
D80.0 ICD10CM Hereditary hypogammaglobulinemia MGI
D80.1 ICD10CM Nonfamilial hypogammaglobulinemia MGI
D80.2 ICD10CM Selective deficiency of immunoglobulin A [IgA] MGI
D80.3 ICD10CM Selective deficiency of immunoglobulin G [IgG] subclasses MGI
D80.4 ICD10CM Selective deficiency of immunoglobulin M [IgM] MGI
D80.5 ICD10CM Immunodeficiency with increased immunoglobulin M [IgM] MGI
D80.6 ICD10CM Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia MGI
D80.7 ICD10CM Transient hypogammaglobulinemia of infancy MGI
D80.8 ICD10CM Other immunodeficiencies with predominantly antibody defects MGI
D80.9 ICD10CM Immunodeficiency with predominantly antibody defects, unspecified MGI
D81 ICD10CM Combined immunodeficiencies MGI
D81.0 ICD10CM Severe combined immunodeficiency [SCID] with reticular dysgenesis MGI
D81.1 ICD10CM Severe combined immunodeficiency [SCID] with low T- and B-cell numbers MGI
D81.2 ICD10CM Severe combined immunodeficiency [SCID] with low or normal B-cell numbers MGI
D81.3 ICD10CM Adenosine deaminase [ADA] deficiency MGI
D81.4 ICD10CM Nezelof's syndrome MGI
D81.5 ICD10CM Purine nucleoside phosphorylase [PNP] deficiency MGI
D81.6 ICD10CM Major histocompatibility complex class I deficiency MGI
D81.7 ICD10CM Major histocompatibility complex class II deficiency MGI
D81.8 ICD10CM Other combined immunodeficiencies MGI
D81.81 ICD10CM Biotin-dependent carboxylase deficiency MGI
D81.810 ICD10CM Biotinidase deficiency MGI
D81.818 ICD10CM Other biotin-dependent carboxylase deficiency MGI
D81.819 ICD10CM Biotin-dependent carboxylase deficiency, unspecified MGI
D81.89 ICD10CM Other combined immunodeficiencies MGI
D81.9 ICD10CM Combined immunodeficiency, unspecified MGI
D82.0 ICD10CM Wiskott-Aldrich syndrome MGI
D82.1 ICD10CM Di George's syndrome MGI
D83 ICD10CM Common variable immunodeficiency MGI
D83.0 ICD10CM Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function MGI
D83.1 ICD10CM Common variable immunodeficiency with predominant immunoregulatory T-cell disorders MGI
D83.2 ICD10CM Common variable immunodeficiency with autoantibodies to B- or T-cells MGI
D83.8 ICD10CM Other common variable immunodeficiencies MGI
D83.9 ICD10CM Common variable immunodeficiency, unspecified MGI
D84.8 ICD10CM Other specified immunodeficiencies MGI
D84.9 ICD10CM Immunodeficiency, unspecified MGI
279.00 ICD9CM Hypogammaglobulinemia, unspecified MGI
279.01 ICD9CM Selective IgA immunodeficiency MGI
279.02 ICD9CM Selective IgM immunodeficiency MGI
279.03 ICD9CM Other selective immunoglobulin deficiencies MGI
279.04 ICD9CM Congenital hypogammaglobulinemia MGI
279.05 ICD9CM Immunodeficiency with increased IgM MGI
279.06 ICD9CM Common variable immunodeficiency MGI
279.09 ICD9CM Other deficiency of humoral immunity MGI
279.10 ICD9CM Immunodeficiency with predominant T-cell defect, unspecified MGI
279.11 ICD9CM Digeorge's syndrome MGI
279.12 ICD9CM Wiskott-aldrich syndrome MGI
279.13 ICD9CM Nezelof's syndrome MGI
279.19 ICD9CM Other deficiency of cell-mediated immunity MGI
279.2 ICD9CM Combined immunity deficiency MGI
279.3 ICD9CM Unspecified immunity deficiency MGI
D80.0 ICD10 D80.0 Hereditary hypogammaglobulinaemia UKB
D80.1 ICD10 D80.1 Nonfamilial hypogammaglobulinaemia UKB
D80.2 ICD10 D80.2 Selective deficiency of immunoglobulin A [IgA] UKB
D80.3 ICD10 D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses UKB
D80.4 ICD10 D80.4 Selective deficiency of immunoglobulin M [IgM] UKB
D80.5 ICD10 D80.5 Immunodeficiency with increased immunoglobulin M [IgM] UKB
D80.6 ICD10 D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinaemia UKB
D80.8 ICD10 D80.8 Other immunodeficiencies with predominantly antibody defects UKB
D80.9 ICD10 D80.9 Immunodeficiency with predominantly antibody defects, unspecified UKB
D81.0 ICD10 D81.0 Severe combined immunodeficiency [SCID] with reticular dysgenesis UKB
D81.1 ICD10 D81.1 Severe combined immunodeficiency [SCID] with low T- and B-cell numbers UKB
D81.8 ICD10 D81.8 Other combined immunodeficiencies UKB
D81.9 ICD10 D81.9 Combined immunodeficiency, unspecified UKB
D82.1 ICD10 D82.1 Di George's syndrome UKB
D83.0 ICD10 D83.0 Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function UKB
D83.1 ICD10 D83.1 Common variable immunodeficiency with predominant immunoregulatory T-cell disorders UKB
D83.2 ICD10 D83.2 Common variable immunodeficiency with autoantibodies to B- or T-cells UKB
D83.8 ICD10 D83.8 Other common variable immunodeficiencies UKB
D83.9 ICD10 D83.9 Common variable immunodeficiency, unspecified UKB
D84.8 ICD10 D84.8 Other specified immunodeficiencies UKB
D84.9 ICD10 D84.9 Immunodeficiency, unspecified UKB
279.1 ICD9 2791 Deficiency of cell-mediated immunity UKB
279.10 ICD9 27910 Deficiency of cell-mediated immunity (di george syndrome) UKB
279.11 ICD9 27911 Deficiency of cell-mediated immunity (wiskott-aldrich syndrome) UKB
279.19 ICD9 27919 Deficiency of cell-mediated immunity (lymphocyte deficiency) UKB
279.2 ICD9 2792 Combined immunity deficiency UKB
279.3 ICD9 2793 Unspecified immunity deficiency UKB

This page is mainly a phenotype dictionary entry. When you are trying to find candidate PRS models, go to the Scores table, search by trait or exposure name, and then use the score-detail and PheWAS pages for model-specific follow-up.

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