Congenital coagulation defects
286.1
Hematopoietic
Both
286-287.99
ICD mappings
| ICD code | Type | Description | Phenome |
|---|---|---|---|
| D66 | ICD10CM | Hereditary factor VIII deficiency | MGI |
| D67 | ICD10CM | Hereditary factor IX deficiency | MGI |
| D68.0 | ICD10CM | Von Willebrand's disease | MGI |
| D68.1 | ICD10CM | Hereditary factor XI deficiency | MGI |
| D68.2 | ICD10CM | Hereditary deficiency of other clotting factors | MGI |
| D69.8 | ICD10CM | Other specified hemorrhagic conditions | MGI |
| 286.0 | ICD9CM | Congenital factor VIII disorder | MGI |
| 286.1 | ICD9CM | Congenital factor IX disorder | MGI |
| 286.2 | ICD9CM | Congenital factor XI deficiency | MGI |
| 286.3 | ICD9CM | Congenital deficiency of other clotting factors | MGI |
| 286.4 | ICD9CM | Von Willebrand's disease | MGI |
| D66 | ICD10 | D66 Hereditary factor VIII deficiency | UKB |
| D67 | ICD10 | D67 Hereditary factor IX deficiency | UKB |
| D68.0 | ICD10 | D68.0 Von Willebrand's disease | UKB |
| D68.1 | ICD10 | D68.1 Hereditary factor XI deficiency | UKB |
| D68.2 | ICD10 | D68.2 Hereditary deficiency of other clotting factors | UKB |
| 286.1 | ICD9 | 2861 Congenital factor ix disorder | UKB |
| 286.2 | ICD9 | 2862 Congenital factor xi disorder | UKB |
This page is mainly a phenotype dictionary entry. When you are trying to find candidate PRS models, go to the Scores table, search by trait or exposure name, and then use the score-detail and PheWAS pages for model-specific follow-up.